The formation of this platelet plug is called primary hemostasis.

这被称初级止过程。

This formation of the platelet plug is called primary hemostasis.

这一过程即初期止。

This is because the process called hemostasis, literally meaning to stop the flow of blood, is impaired.

这是因病患者止过程受损，即功能出现障碍。

People who suffer from disorders related to hemostasis may have trouble with unwanted clotting, or the inability to form clots.

患有与止相关疾病人可能会有不必要或无法形成块问题。

The formation of the platelet plug is called primary hemostasis.

小板栓子形成叫做一期止。

Normally, protein C and protein S are 2 of many proteins or enzymes that regulate the complex process called hemostasis.

通常，蛋白C和蛋白S是能调节止这一复杂过程许多蛋白和酶中两种。

The main role of protein C and protein S is to prevent excess coagulation, or fibrin formation, during secondary hemostasis.

蛋白C和蛋白S主要作用是在二期止时防止过度（即纤维蛋白形成过多）。

So, it has a whole system in place to prevent you from losing too much of it, through a process known as hemostasis.

所以，它有一个完整系统来防止你失去太多，通过一个被称止过程。

The second factor is a state of hypercoagulation, where altered amounts of clotting factors increase primary or secondary hemostasis.

第二个因素是高状态，高状态下因子数量增多，会增强初期或二期。

Now, a mimic of hemophilia A is von Willebrand disease, which is an inherited problem with primary hemostasis caused by a deficiency of von Willebrand factor.

还有一种病A，即管性病，是一种遗传性初级止障碍，由管性病因子（vWF）缺乏引起。

In the family of disorders known as hemophilia, a patient can usually complete the first two steps of hemostasis just fine, but they can't make an effective fibrin clot.

在被称病疾病家族中，病人通常可以很好地完成止前两个步骤，但是他们不能制造有效纤维蛋白块。

So these steps leading up to fibrin reinforcement of the platelet plug make up the process called secondary hemostasis and results in a hard clot at the site of the injury.

这一加强小板栓强度过程即二期止，最终使得伤口上栓很牢固。

In most cases of hemophilia there is a decrease in the amount or function of one or more of the clotting factors that makes secondary hemostasis less effective and allows more bleeding to occur.

在大多数病中，都有一种或多种因子在数量上减少或功能上减弱，使次级止过程功效下降，而出更多。

To make things worse, as the clots are broken down through fibrinolysis, fibrin degradation products are released into the circulation and these interfere with platelet aggregation and clot formation, making hemostasis even more difficult.

更糟是，当块通过纤溶崩解时，纤维蛋白降解产物释放入液循环，干扰小板聚集和块形成，导致更加困难。