1.Methylmalonic acidemia is an inherited metabolic disorder,which is caused by deficiency of methylmalonyl-coenzyme A mutase or its cofactor adenosylcobalamin.

1.基丙二酸血症是基丙二酰辅酶A变位酶或其辅酶苷钴胺素缺陷所致的一种遗传疾病。

2.Prosthetic enzyme of mutase, catalyze reactions of group, mainly methyl, metachoresis in the interior of substrate molecule.

2.变位酶的辅酶，催化底物分子内基团(主要为基)的变位反应。