Incontinentia pigmenti is a rare genodermatosis that usually affects female infants.The associated abnormalities involve ocular, dental, skeletal and central nervous systems.
The episode began with two attacks of generalized tonic-clonic seizures, fever and consciousness disturbance, followed by urinary incontinence and paraplegia with hyporeflexia.
We present a 29 year-old male with a history of coumadin therapy for deep vein thrombosis who developed exsanguinating lower back pain and progressive neurological deterioration.