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But without gangliosides the txansparency of supernatant of injuried control erythrocytes is only 13.4% of the nounal value.The injuried erythrocytes shriek with spines on their surface.

而损伤对照组上清透光度的13.4%,红细胞胞体缩小,成棘形红细胞。

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Osmosis-遗传

All right, as a quick recap, Tay-Sachs disease is a lysosomal storage disease that results in a buildup of GM2 ganglioside in neurons of the central nervous system.

好,快速回顾下:Tay-Sachs是一种溶酶体,能引中枢元中GM2

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Osmosis-遗传

This enzyme normally breaks down a lipid called GM2 ganglioside.

HEX-A正常情况下能降解一种叫做GM2脂的脂质。

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